Basic characteristics of cerebellar patients
| Patient | Diagnosis | Age (years) | Sex | Duration (years) | SARA | ICARS |
|---|---|---|---|---|---|---|
| 1 | SCA14 | 58 | M | 17 | 21 | 33 |
| 2 | ADCA III | 55 | F | 22 | 17 | 30 |
| 3 | ADCA III | 25 | M | 2 | 6 | 9 |
| 4 | SAOA | 70 | M | 15 | 22 | 48 |
| 5 | ADCA III | 56 | M | 19 | 24 | 44 |
| 6 | SCA6 | 58 | F | 8 | 19 | 46 |
| 7 | SAOA | 65 | M | 17 | 17 | 30 |
| 8 | ADCA III | 30 | F | 1 | 7 | 16 |
| 9 | SCA8 | 60 | M | 9 | 15 | 23 |
| 10 | SAOA | 67 | F | 14 | 16 | 31 |
| 11 | SAOA | 55 | F | 5 | 19 | 22 |
| 12 | SCA6 | 62 | M | 7 | 17 | 28 |
| 13 | ADCA III | 56 | F | 15 | 12 | 19 |
| 14 | SAOA | 66 | M | 2 | 18 | 26 |
| 15 | SCA6 | 52 | M | 15 | 6 | 15 |
| 16 | SAOA | 59 | F | 9 | 12 | 28 |
| 17 | SCA6 | 39 | F | 1 | 12 | 21 |
| 18 | SCA8 | 62 | F | 12 | 4 | 5 |
| 19 | SCA6 | 53 | F | Presymptomatic | 1 | 3 |
| 20 | SCA6 | 65 | M | 27 | 15 | 30 |
Listed are age and disease duration at examination; SCA6, SCA8, SCA14, spinocerebellar ataxia types 6, 8, and 14; ADCA III, autosomal dominant cerebellar ataxia type III; SAOA, sporadic adult-onset ataxia of unknown etiology. Severity of ataxia was rated using the ICARS and the SARA. Total SARA and ICARS scores are given. Maximum ICARS score is 100; maximum SARA score is 40 (Trouillas et al., 1997; Schmitz-Hübsch et al., 2006).