Table 1

Hippocampus CA1 and cerebral cortex tissue samples of HD patients

IDRegionPathologic diagnosisGenderAge (years)CAG repeatsPMD (h:min)*
CS-497CA1ControlM82 02:30
CS-1694CA1ControlM58 05:00
CS-1858CA1ControlF83 07:30
CS-1870CA1ControlF97 07:20
CS-1888CA1ControlF93 05:30
CS-1937CA1ControlF83 07:33
CS-1949CA1ControlM86 07:25
CS-1193CA1HD, Vonsattel grades 3–4M55-07:00
CS-1294CA1HD, Vonsattel grade 3M5345 ± 207:00
CS-1334CA1HD, Vonsattel grade 1M7340 ± 207:00
CS-1438CA1HD, Vonsattel grade 3M854005:30
CS-1630CA1HD, Vonsattel grade 2M764106:00
CS-1638CA1HD, Vonsattel grade 2M72-13:10
CS-1844CA1HD, Vonsattel grade 2F694315:30
CS-1874CA1HD, Vonsattel grade 3M564304:30
CS-1875CA1HD, Vonsattel grades 2–3M843908:00
CS-1933CA1HD, Vonsattel grade 2F864012:20
810CortexControlF81 23:30
1679CortexControlF90 12:20
1697CortexControlM78 06:00
1870CortexControlF97 07:20
1937CortexControlF83 07:33
1949CortexControlM86 07:25
1980CortexHD, Vonsattel grade 3F69-12:30
1875CortexHD, Vonsattel grades 2–3M843908:00
1844CortexHD, Vonsattel grade 2F694315:30
1638CortexHD, Vonsattel grade 2M72-13:10
1630CortexHD, Vonsattel grade 2M763806:00
909CortexHD, Vonsattel grade 4M604313:30
  • Details of human postmortem samples used for Western blotting to analyze protein levels of TCF4. All samples received from the Neurologic Tissue Bank-Biobanc located at the University of Barcelona School of Medicine. *PMD, postmortem delay.